[MIM 192 350];

Acronym for Vertebral anomalies, Anal atresia, Cardiac defects, Tracheoesophageal fistula and/or Esophageal atresia, Renal & Radial anomalies and Limb defects

See also : esophageal atresia

Prevalence is estimated at 1/10.000 to 1/40,000. Association, to varying degrees, of malformations according to the acronym of the syndrome.

A rare form of VATER is transmitted on a recessive mode or X-linked and include hydrocephalus (VACTER - H) [MIM 276 950, 314 390 ]

Anesthetic implications:

according to the importance of the associated malformations: intubation, vascular access, difficult neuraxial anesthesia

References: 

-         Hilton G, Mihm F, Butwick A. 
Anesthetic management of a parturient with VACTERL association undergoing Cesarean delivery.
Can J Anesth 2013; 60: 570-6.

Updated: September 2018