Extremely rare. Eosinophilic fasciitis  characterized by:

-        damage to the joints (especially the elbows and hands)

-        and induration of the superficial tissues of the limbs sometimes accompanied by localized depigmentation.

Sometimes: blood hypereosinophilia, hepatosplenomegaly, Raynaud's syndrome. Muscular involvement can be combined.

It is due to  lymphoplasmacytic infiltration of the fascia and subcutaneous tissue.

Treatment: transient corticosteroid therapy; immunosuppression in case of corticoresistance

Anesthetic implications:

corticosteroids, difficult peripheral venous access.

References : 

•        Hamdi W, Haouel M, Chaabouni S et al. 
  Syndrome de Shulman chez l’enfant. 
  Arch Pédiatr 2012 ; 19 : 180-3.

Updated: September 2018