Acronym for Sebaceous nevus syndrome, CNS malformations, Aplasia cutis congenita, Limbal dermoid, and Pigmented nevus.

Extremely rare. It could be a variant of Schimmelpenning-Feuerstein-Mims syndrome (see this term).

Association of:

-        an important sebaceous nevus in the head and neck region

-        an aplasia cutis congenita (see this term) at the level of the scalp

-        dermoid tumors

-        central nervous system abnormalities: mainly melanosis

-        a giant pigmented nevus

Anesthetic implications:

risk of epilepsy or of cerebral aneurysm

References : 

-        Lam J, Dohil MA, Eichenfield LF, Cunningham BB.
SCALP syndrome: sebaceous nevus syndrome, CNS malformations, aplasia cutis congenita, limbal dermoid, and pigmented nevus (giant congenital melanocytic nevus) with neurocutaneous melanosis : a distinct syndrome entity.
J Am Acad Dermatol 2008; 58: 884-8.

-        Tateosan VS, Smith J, Licata S.
Large intracranial aneurysms in a 2-month-old female.
Anesthesiology 2017, in press

Updated: September 2017