Pulmonary capillaritis, pauci-immune
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Rare. It is a vascularitis involving the small vessels and limited to the lung; its only manifestation is alveolar hemorrhage in patients aged 18 to 35 years. It is a possible cause of idiopathic pulmonary hemosiderosis (see this term) in children.
Diagnosis: pulmonary biopsy.
Anesthetic implications:
References:
- Fullmer JJ, Langston C, Dishop MK, Fan LL.
Pulmonary capillaritis in children: a review of eight cases with comparison to other alveolar hemorrhage syndromes.
J Pediatr 2010; 23: 25-31.
Updated: January 2021