Pectus carinatum
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(keel chest, pigeon chest)
Congenital deformation of the chest characterized by a forward chondrosternal prominence. The sternum has a particular tipped shape, resembling the keel of a boat. Much rarer than pectus excavatum (1/4000 births) and often associated with other disorders (Marfan's syndrome, heart and/or musculoskeletal abnormalities, scoliosis). It could be caused by an excessive growth of the chondro-sternal cartilage.
There is an even rarer form of sternal protrusion, in the upper part of the sternum, called “pectus arcuatum”.
Treatment may be:
- orthotic, before puberty: external dynamic compression (braces)
- surgical: either cartilage removal, or insertion of two metal bars (surgically removed later), to re-shape the sternum as for pectus excavatum. Anesthetic management and postoperative management are similar to those of the funnel chest surgery.
Anesthetic implications:
preoperative echocardiography.
References :
- Robicsek F, Watts LT.
Pectus carinatum.
Thorac Surg Clin 2010; 20:563-74.
- Martinez-Ferro M, Fraire C, Bernard S.
Dynamic compression system for the correction of pectus carinatum.
Semin Pediatr Surg. 2008;17:194-200
- Robicsek F, Watts LT, Fokin AA.
Surgical repair of pectus excavatum and carinatum.
Semin Thorac Cardiovasc Surg 2009; 21:64-75.
- Kim S, Idowu O.
Minimally invasive thoracoscopic repair of unilateral pectus carinatum.
J Pediatr Surg 2009; 44:471-4.
Updated: November 2018