Parry Romberg, syndrome
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see also linear scleroderma
Very rare. Sporadic. Progressive atrophy of the skin, soft tissue and bony structures of half of the face. Affection often begins around puberty and during 3-5 years before stabilizing. Neurological signs may be associated: Horner's syndrome, ataxia, migraine, trigeminal neuralgia, epilepsy.
Anesthetic implications:
risk of difficult mask ventilation: fullfill the gap between the face and the mask with humidified gauze pads or modeling clay; risk of difficult intubation; risk of pulmonary fibrosis: chest XRay; one case of acute rhabdomyolysis with cardiac arrest has been reported following the use of succinylcholine. Beware of the possible ocular and neurological complications.
References :
- Tritakarn T, Teeratchanan T.
Acute rhabdomyolysis and cardiac arrest following succinylcholine in a patient with Parry-Romberg syndrome.
Anaesth Intens Care 2011; 39: 135-6.
- Karkar AM, Hong T.
Anesthesia management of a patient with Parry-Romberg syndrome: a case report.
J Anesth Clin Res 2014; 5: 397-9
- Jayaram K, Gurala I, Ramachandran G.
Difficult mask ventilation made easy: three cases of Parry Romberg syndrome.
Indian J Anaesth 2016; 60: 280-3.
Updated: November 2018