Neurofibromatoses

 Riccardi's classification


Type I

NF1

von Recklinghausen disease

Type II

NF2

acoustic neurofibromatosis

Type III

NF3

mixed neurofibromatosis, NF1 et NF2, orschwannomatosis

Type IV

NF4

unclassifiable forms

Type V

NF5

segmental neurofibromatosis

Type VI

NF6

isolated café-au-lait spots

Type VII

NF7

late onset neurofibromatosis (> 30 years)


NF1- like

neurofibromatosis 1-like or Legius syndrome


NF-NOS

badly specified forms limited to the

digestive tract, 

Noonan-NF1 syndrome

schwannomatosis or neurilemmomatosis