(Intravascular papillary endothelial hyperplasia)

Rare benign tumor of the cutaneous and subcutaneous vessels. It is characterized by an excessive and papillary proliferation of the endothelial cells in one or more vessels, following a thrombotic event. It is sometimes painful. It is mainly found in adults (without a specific age), and is preferentially located in the face and limbs, sometimes in the brain or the adrenal glands. Cases have been described in children. The differential clinical diagnosis of this tumor is the angiosarcoma. Only the surgical exeresis with anatomopathological examination can differentiate them.

There are three types:

• pure form (56 %) developing in the lumen of a dilated vessel, usually a vein
• secondary form (40 %) developing in a pre-existing lesion: aneurysm, arteriovenous malformation, hemangioma, pyogenic granuloma
• extravascular form (4 %) developing from a hematoma.

Anesthetic implications:

depending on the location of the tumor.

References :

-        Liné A, Sanchez J, Jayyosi L, Birembaut P, Ohl X, Poli-Mérol M-L, François C.
Papillary endothelial hyperplasia (Masson’s tumor) in children.
Ann Chir Plast Esthet 2017; 62: 232-7.

Updated: April 2021