Lown-Ganong-Levine, syndrome
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(Short PR - normal QRS syndrome)
Incidence : less than 1/106. Sporadic or autosomal dominant inheritance. Preexcitation syndrome by the bundle of James, without δ wave, unlike Wolff-Parkinson-White syndrome.
ECG : short PR (≤ 120 msec) with normal QRS.
Clinical picture: episodes of paroxysmal tachycardia.
Anesthetic implications:
monitoring of the ECG. In case of atrial fibrillation, verapamil and digoxin are contraindicated.
References :
- Villain E.
Tachycardies jonctionnelles réciproques et voies accessoires. p 55-64
In Les troubles du rythme cardiaque chez l’enfant. Kachaner J et Villain E, Médecine-Sciences Flammarion, 2006.
Updated: February 2019