MIM 236 110]

(Holzgreve-Wagner-Rehder syndrome)

 Prevalence: < 1/200,000. Malformative syndrome of genetic origin, probably with autosomal recessive transmission. It associates  polydactyly, palatine division with persistence of bucco-pharyngeal membrane, birth defects and growth retardation. There is sometimes an associated renal agenesis (Potter syndrome).

Anesthetic implications: 

difficult intubation, risk of aspiration; renal failure in some forms.

References : 

Updated: March 2019