Rare. Hemiatrophy of one cerebral hemisphere which can result in facial asymmetry, convulsions, contralateral hemiparesis, mental retardation and learning disabilities.

The causes may be

-         congenital: a perinatal vascular accident; neuroimaging then shows a shift of the heterolateral structures to the affected side.

-         acquired: due to trauma, ischemia, infection or unilateral cerebral hemorrhage.

Anesthetic implications: 

epilepsy, mental retardation, verify the absence of hypertension and thrombophilia. Risk of difficult mask ventilation or intubation, specially if the right side is involved.

References : 

-         Roy K, Talukdar A, ray A, Pal P. 
Dyke-Davidoff-Masson syndrome-like picture in a case of Takayasu arteritis : an enigma.
BMJ Case Reports 2012 doi 10.1136/bcr-2012-006669

-        El-Bahri Ben Mrad F, Mrabet H, Ben Sghaier R, Mrabet A. 
Syndrome de Dyke-Davidoff-Masson: à propos de deux observations.  
J Neuroradiol 2005; 32: 50-3. 

-        Thakkar PA, Dave RH.
Dyke-Davidoff-Mason Syndrome : A rare cause of cerebral hemiatrophy in children.
J Pediatr Neurosci. 2016 ; 11 :252-4

Updated: March 2021