Cacchi-Ricci, disease

(Medullary sponge kidney)

The most frequent congenital malformation of the kidney. Unknown origin: there are familial cases. It consists of precaliceal ectasies of the renal tubules; it remains  asymptomatic for a long time but small precalyceal lithiasis can develop and result in repeated urinary tract infections. The malformation can be bilateral (70%), unilateral or limited to a segment of a kidney. 


Possibly associated problems:

-         hypercalciuria

-         hypocitraturia

-         Caroli disease (see this term)


Anesthetic implications:

monitor the renal function, ensure optimal hydration in the perioperative period.


References : 


Updated: November 2019