Extremely rare. 

Association of 

-         a distal aorto-pulmonary window with a right pulmonary artery arising from the ascending aorta

-         aplasia/hypoplasia of the aortic arch (type B) with a persistent ductus arteriosus

-         an intact interventricular septum

Anesthetic implications: 

complex heart disease to be corrected or palliated in the neonatal period

References : 

• Abbruzzeze PA, Merlo M, Chiappa E, Bianco R, Ferrero F, Cappone CM. 
  Berry syndrome, a complex aortopulmonary malformation: one-stage repair in a neonate. 
  Ann Thor Surg 1997; 64: 1167-9. 
• Park SY, Joo HC, Youn YN, Park YH et al.
  Berry syndrome : two cases of successful surgical repair.
  Circ J 2008 ; 72 : 492-5.

Updated: November 2019